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1

Detection and Isolation of Gene-Corrected Cells in Gaucher Disease Via a Fluorescence-Activated Cell Sorter Assay for Lysosomal Glucocerebrosidase Activity

Lorincz, Matthew, Herzenberg, Leonard A., Diwu, Zhenjun, Barranger, John A., Kerr, William G.

Journal:

Année:

1997

Fichier:

PDF, 270 KB

1997

2

Fabry Disease in Genetic Counseling Practice: Recommendations of the National Society of Genetic Counselors

Robin L. Bennett, Kimberly A. Hart, Erin O'Rourke, John A. Barranger, Jack Johnson, Kay D. MacDermot, Gregory M. Pastores, Robert D. Steiner, Ravi Thadhani

Journal:

Journal of Genetic Counseling

Année:

2002

Langue:

english

Fichier:

PDF, 159 KB

english, 2002

3

An improved high-throughput dried blood spot screening method for Gaucher disease

Petra Olivova, Emmaline Cullen, Mariah Titlow, Helmut Kallwass, John Barranger, Kate Zhang, Joan Keutzer

Journal:

Clinica Chimica Acta

Année:

2008

Langue:

english

Fichier:

PDF, 222 KB

english, 2008

4

SPIE Proceedings [SPIE San Dieg - DL Tentative - San Diego, CA (Sunday 1 July 1990)] Optical Testing and Metrology III: Recent Advances in Industrial Optical Inspection - Two-dimensional surface strain measurement based on a variation of Yamaguchi's laser-speckle strain gauge

Barranger, John P., Grover, Chander P.

Année:

1991

Langue:

english

Fichier:

PDF, 275 KB

english, 1991

5

Guidance on the use of miglustat for treating patients with type 1 Gaucher disease

Neal J. Weinreb, John A. Barranger, Joel Charrow, Gregory A. Grabowski, Henry J. Mankin, Pramod Mistry

Journal:

American Journal of Hematology

Année:

2005

Langue:

english

Fichier:

PDF, 101 KB

english, 2005

6

Normal pyruvate dehydrogenase complex activity in patients with Friedreich's ataxia

George Constantopoulos, Charles S. C. Chang, John A. Barranger

Journal:

Annals of Neurology

Année:

1980

Langue:

english

Fichier:

PDF, 405 KB

english, 1980

7

Reply

R. N. Nishimura, K. G. Ishak, R. Reddick, R. Porter, S. James, John A. Barranger

Journal:

Annals of Neurology

Année:

1981

Langue:

english

Fichier:

PDF, 121 KB

english, 1981

8

Type 2 and type 3 Gaucher disease: A morphological and biochemical study

Dr Edward M. Kaye, M. David Ullman, Edward R. Wilson, John A. Barranger

Journal:

Annals of Neurology

Année:

1986

Langue:

english

Fichier:

PDF, 1.23 MB

english, 1986

9

B-scan echo-amplitude measurement in patients with diffuse infiltrative liver disease

Thomas H. Shawker, Beckie Moran, Melvin Linzer, Stephen I. Parks, Stephen P. James, F. Wayne Stromeyer, John A. Barranger

Journal:

Journal of Clinical Ultrasound

Année:

1981

Langue:

english

Fichier:

PDF, 1.54 MB

english, 1981

10

The distribution of glucocerebroside in the liver of patients with Gaucher's disease

Andrew E. Gal, Peter G. Pentchev, John A. Barranger, James M. Dambrosia, Roscoe O. Brady

Journal:

Analytical Biochemistry

Année:

1979

Langue:

english

Fichier:

PDF, 446 KB

english, 1979

11

Nonenzymatic decarboxylation of pyruvate

George Constantopoulos, John A. Barranger

Journal:

Analytical Biochemistry

Année:

1984

Langue:

english

Fichier:

PDF, 476 KB

english, 1984

12

Purification of β-glucocerebrosidase by preparative-scale high-performance liquid chromatography: The use of ethylene glycol-containing buffers for chromatography of hydrophobic glycoprotein enzymes

Gary J. Murray, Richard J. Youle, Samuel E. Gandy, Gregory C. Zirzow, John A. Barranger

Journal:

Analytical Biochemistry

Année:

1985

Langue:

english

Fichier:

PDF, 1.04 MB

english, 1985

13

A procedure for the rapid purification in high yield of human glucocerebrosidase using immunoaffinity chromatography with monoclonal antibodies

Johannes M.F.G. Aerts, Wilma E. Donker-Koopman, Gary J. Murray, John A. Barranger, Joseph M. Tager, AndréW. Schram

Journal:

Analytical Biochemistry

Année:

1986

Langue:

english

Fichier:

PDF, 831 KB

english, 1986

14

Identification of the binding and activating sites of the sphingolipid activator protein, saposin C, with glucocerebrosidase

Solly Weiler, John M. Tomich, Yasuo Kishimoto, John S. O'Brien, John A. Barranger

Journal:

Protein Science

Année:

1995

Langue:

english

Fichier:

PDF, 864 KB

english, 1995

15

Position of the sulfhydryl group and the disulfide bonds of human glucocerebrosidase

Yonih Lee, Haruyuki Kinoshita, Gary Radke, Solly Weiler, John A. Barranger, John M. Tomich

Journal:

The Protein Journal

Année:

1995

Langue:

english

Fichier:

PDF, 1.08 MB

english, 1995

16

Saposins (Sphingolipid Activator Proteins) in the Twitcher Mutant Mouse

Hidenari Shigematsu, Satoshi Morimoto, Yasuo Kishimoto, Solly Weiler, John Tomich, John Barranger, Mitsuko Shinohara, Andrew M. Yeager, John S. O'Brien

Journal:

Journal of Neurochemistry

Année:

1990

Langue:

english

Fichier:

PDF, 370 KB

english, 1990

17

Gene Transfer Approaches to the Lysosomal Storage Disorders

John A. Barranger, Erin O. Rice, William P. Swaney

Journal:

Neurochemical Research

Année:

1999

Langue:

english

Fichier:

PDF, 1.76 MB

english, 1999

18

Organomegaly and histopathology in an animal model of mucopolysaccharidosis induced by suramin

Sandra Rees, George Constantopoulos, John A. Barranger, Roscoe O. Brady

Journal:

Naunyn-Schmiedeberg's Archives of Pharmacology

Année:

1982

Langue:

english

Fichier:

PDF, 4.31 MB

english, 1982

19

Immunological studies on lysosomal sphingomyelinase: Identification of a 28 000-Da component deficient in urine from patients with Niemann-Pick disease types A and B

André W. Schram, Marianne Dreissen, Johan Bastiaannet, Wilma E. Donker-Koopman, Elisabeth M. Brouwer-Kelder, Gabriele Weitz, John A. Barranger, Konrad Sandhoff, Joseph M. Tager

Journal:

Bioscience Reports

Année:

1984

Langue:

english

Fichier:

PDF, 841 KB

english, 1984

20

Synthesis and characterization of a bioactive 82-residue sphingolipid activator protein, saposin C

Solly Weiler, Wulf Carson, Yonih Lee, David B. Teplow, Yasuo Kishimoto, John S. O’Brien, John A. Barranger, John M. Tomich

Journal:

Journal of Molecular Neuroscience

Année:

1993

Langue:

english

Fichier:

PDF, 1.05 MB

english, 1993

21

Skeletal manifestations of Gaucher's disease

Behram Pastakia, Anne C. Brower, Victoria H. Chang, John A. Barranger

Journal:

Seminars in Roentgenology

Année:

1986

Langue:

english

Fichier:

PDF, 10.65 MB

english, 1986

22

Centrifugal enhancement of retroviral mediated gene transfer

Alfred B. Bahnsonz, James T. Dunigan, Bora E. Baysal, Trina Mohney, R. Wayne Atchison, Maya T. Nimgaonkar, Edward D. Ball, John A. Barranger

Journal:

Journal of Virological Methods

Année:

1995

Langue:

english

Fichier:

PDF, 977 KB

english, 1995

23

Conditions affecting the activity of glucocerebrosidase purified fom spleens of control subjects and patients with type 1 Gaucher disease

Johannes M.F.G. Aerts, M.Clara Sa Miranda, Elidabeth M. Brouwer-Kelder, Sonja Van Weely, John A. Barranger, Joseph M. Tager

Journal:

Biochimica et Biophysica Acta (BBA) - Protein Structure and Molecular Enzymology

Année:

1990

Langue:

english

Fichier:

PDF, 852 KB

english, 1990

24

Comparison of methods for retroviral mediated transfer of glucocerebrosidase gene to CD34+ hematopoietic progenitor cells

Nobuaki Takiyama, Trina Mohney, William Swaney, Alfred B. Bahnson, Erin Rice, Margaret Beeler, Sherrie Scheirer-Fochler, Edward D. Ball, John A. Barranger

Journal:

European Journal of Haematology

Année:

1998

Langue:

english

Fichier:

PDF, 530 KB

english, 1998

25

Activity of glucocerebrosidase in extracts of different cell types from type 1 Gaucher disease patients

M. Clara Sa Miranda, Johannes M. F. G. Aerts, Rui Pinto, Augusta Fontes, Lucia Wanzeller de Lacerda, Sonja van Weely, John Barranger, Joseph M. Tager

Journal:

Clinical Genetics

Année:

1990

Langue:

english

Fichier:

PDF, 644 KB

english, 1990

26

Gaucher disease: studies of phenotype, molecular diagnosis and treatment

Erin O. Rice, Theodore E. Mifflin, Sameer Sakallah, Robert E. Lee, Carol A. Sansieri, John A. Barranger

Journal:

Clinical Genetics

Année:

1996

Langue:

english

Fichier:

PDF, 796 KB

english, 1996

27

Monoclonal Antibodies against Human β-Glucocerebrosidase

Ruud A. BARNEVELD, Frans P. W. TEGELAERS, Edward I. GINNS, Pim VISSER, Elly A. LAANEN, Roscoe O. BRADY, Hans GALJAARD, John A. BARRANGER, Arnold J. J. REUSER, Joseph M. TAGER

Journal:

Année:

1983

Langue:

english

Fichier:

PDF, 589 KB

english, 1983

28

The occurrence of two immunologically distinguishable β-glucocerebrosidases in human spleen

Johannes M. F. G. AERTS, Wilma E. DONKER-KOOPMAN, Martin K. VAN DER VLIET, Lisbeth M. V. JONSSON, Edward I. GINNS, Gary J. MURRAY, John A. BARRANGER, Joseph M. TAGER, André W. SCHRAM

Journal:

Année:

1985

Langue:

english

Fichier:

PDF, 1014 KB

english, 1985

29

Studies on the turnover of glucocerebrosidase in cultured rat peritoneal macrophages and normal human fibroblasts

Pijush K. DAS, Gary J. MURRAY, John A. BARRANGER

Journal:

Année:

1986

Langue:

english

Fichier:

PDF, 621 KB

english, 1986

30

Biosynthesis and maturation of glucocerebrosidase in Gaucher fibroblasts

Lisbeth M. V. JONSSON, Gary J. MURRAY, Susan H. SORRELL, Anneke STRIJLAND, Johannes F. G. M. AERTS, Edward I. GINNS, John A. BARRANGER, Joseph M. TAGER, André W. SCHRAM

Journal:

Année:

1987

Langue:

english

Fichier:

PDF, 999 KB

english, 1987

31

Relationship between the two immunologically distinguishable forms of glucocerebrosidase in tissue extracts

Johannes M. F. G. AERTS, Wilma E. DONKER-KOOPMAN, Coos van LAAR, Stanley BRUL, Gary J. MURRAY, David A. WENGER, John A. BARRANGER, Joseph M. TAGER, André W. SCHRAM

Journal:

Année:

1987

Langue:

english

Fichier:

PDF, 733 KB

english, 1987

32

Signal sequence and DNA-mediated expression of human lysosomal α-galactosidase A

Shoji TSUJI, Brian M. MARTIN, David C. KASLOW, Barbara R. MIGEON, Prabhakara V. CHOUDARY, Barbara K. STUBBLEFLIED, June A. MAYOR, Gary J. MURRAY, John A. BARRANGER, Edward I. GINNS

Journal:

Année:

1987

Langue:

english

Fichier:

PDF, 635 KB

english, 1987

33

Function of oligosaccharide modification in glucocerebrosidase, a membrane-associated lysosomal hydrolase

Sonja VAN WEELY, Johannes M. F. G. AERTS, Marinella B. VAN LEEUWEN, Judith C. HEIKOOP, Wilma E. DONKER-KOOPMAN, John A. BARRANGER, Joseph M. TAGER, André W. SCHRAM

Journal:

Année:

1990

Langue:

english

Fichier:

PDF, 1.13 MB

english, 1990

34

Gene therapy for metachromatic leukodystrophy

TOYA OHASHI, KAZUHIKO WATABE, YUMI SATO, IZUMU SAITO, JOHN A BARRANGER, REUBEN MATALON, YOSHIKATSU ETO

Journal:

Pediatrics International

Année:

1996

Langue:

english

Fichier:

PDF, 785 KB

english, 1996

35

Chronic airflow obstruction in Fabry's disease

David M. Rosenberg, Victor J. Ferrans, Jack D. Fulmer, Bruce R. Line, John A. Barranger, Roscoe O. Brady, Ronald G. Crystal

Journal:

The American Journal of Medicine

Année:

1980

Langue:

english

Fichier:

PDF, 2.13 MB

english, 1980

36

Gaucher's disease in a patient with chronic active hepatitis

Shutish C. Patel, Gary L. Davis, John A. Barranger

Journal:

The American Journal of Medicine

Année:

1986

Langue:

english

Fichier:

PDF, 1.53 MB

english, 1986

37

Isolation of cDNA clones for human β-glucocerebrosidase using the λgtll expression system

Edward I. Ginns, Prabhakara V. Choudary, Brian M. Martin, Suzanne Winfield, Barbara Stubblefield, June Mayor, Denise Merkle-Lehman, Gary J. Murray, Lisa A. Bowers, John A. Barranger

Journal:

Biochemical and Biophysical Research Communications

Année:

1984

Langue:

english

Fichier:

PDF, 1.07 MB

english, 1984

38

The implications of multiple forms of phenylalanine hydroxylase in phenylketonuria and related diseases of phenylalanine metabolism

John A. Barranger

Journal:

Biochemical Medicine

Année:

1976

Langue:

english

Fichier:

PDF, 1.82 MB

english, 1976

39

Studies of the isoenzymes of phenylalanine hydroxylase in humans

Charles E. Parker, John Barranger, Rebecca Newhouse, Samuel Bessman

Journal:

Biochemical Medicine

Année:

1977

Langue:

english

Fichier:

PDF, 251 KB

english, 1977

40

Pyruvate decarboxylating activity in extracts from pigeon liver acetone powder

George Constantopoulos, John A. Barranger

Journal:

Biochemical Medicine

Année:

1983

Langue:

english

Fichier:

PDF, 318 KB

english, 1983

41

Molecular weight characterization of β-d-glucocerebrosidase in mononuclear white blood cells in Gaucher's disease

Samuel Pirruccello, John A. Barranger, Norman W. Barton, Roscoe O. Brady, Edward I. Ginns

Journal:

Biochemical Medicine

Année:

1984

Langue:

english

Fichier:

PDF, 592 KB

english, 1984

42

Relationship between production and release of lymphocyte-activating factor (interleukin 1) by murine macrophages: I. Effects of various agents

Igal Gery, Philip Davies, Julia Derr, Nancy Krett, John A. Barranger

Journal:

Cellular Immunology

Année:

1981

Langue:

english

Fichier:

PDF, 709 KB

english, 1981

43

125Iodine labeling of β-hexosaminidase a without modifying its properties

John W. Kusiak, John A. Barranger

Journal:

Clinica Chimica Acta

Année:

1979

Langue:

english

Fichier:

PDF, 365 KB

english, 1979

44

The diagnosis of type A and type B niemann-pick disease and detection of carriers using leukocytes and a chromogenic analogue of sphingomyelin

Andrew E. Gal, Roscoe O. Brady, John A. Barranger, Peter G. Pentchev

Journal:

Clinica Chimica Acta

Année:

1980

Langue:

english

Fichier:

PDF, 254 KB

english, 1980

45

Reclassification of previously reported cases of mucopolysaccharidosis type IS to mucopolysaccharidosis type VI

George Constantopoulos, Daniel W. Stowens, John A. Barranger

Journal:

Clinica Chimica Acta

Année:

1982

Langue:

english

Fichier:

PDF, 170 KB

english, 1982

46

Determination of Gaucher's disease phenotypes with monoclonal antibody

Edward I. Ginns, Franz P.W. Tegelaers, Ruud Barneveld, Hans Galjaard, Arnold J.J. Reuser, Roscoe O. Brady, Joseph M. Tager, John A. Barranger

Journal:

Clinica Chimica Acta

Année:

1983

Langue:

english

Fichier:

PDF, 377 KB

english, 1983

47

Deficient activity of glucocerebrosidase in urine from patients with type 1 Gaucher disease

Johannes M.F.G. Aerts, Wilma E. Donker-Koopman, Maarten Koot, John A. Barranger, Joseph M. Tager, AndréW. Schram

Journal:

Clinica Chimica Acta

Année:

1986

Langue:

english

Fichier:

PDF, 637 KB

english, 1986

48

Lysosomal enzymes in chorionic villi, cultured amniocytes, and cultured skin fibroblasts

Mark I. Evans, Carol Moore, Edwin H. Kolodny, Martha Casassa, Joseph D. Schulman, Ellen J. Landsberger, Evelyn M. Karson, Andrew D. Dorfmann, John W. Larsen Jr., John A. Barranger

Journal:

Clinica Chimica Acta

Année:

1986

Langue:

english

Fichier:

PDF, 324 KB

english, 1986

49

Glucocerebrosidase deficiency and lysosomal storage of glucocerebroside induced in cultured macrophages

Pijush K. Das, Gary J. Murray, Andrew E. Gal, John A. Barranger

Journal:

Experimental Cell Research

Année:

1987

Langue:

english

Fichier:

PDF, 1.62 MB

english, 1987

50

The uptake of agalacto-glucocerebrosidase by rat hepatocytes and kupffer cells

Clifford J. Steer, F.Scott Furbish, John A. Barranger, Roscoe O. Brady, E.Anthony Jones

Journal:

Année:

1978

Langue:

english

Fichier:

PDF, 356 KB

english, 1978